Behçet disease: evaluation of clinical manifestations in Turkish children
نویسندگان
چکیده
Results In 54 patients the mean age at the first symptom was 117.50±45.20 months. BD was suspected at a mean age of 143.56±39.63 months. The mean delay between the first symptom and BD suspicion was 27.36±27.15 months. The most common manifestations were oral ulcer 96.3% (n=52), uveitis 46.3% (n=25), genital ulcer 37% (n=20), pustuler lesion 37% (n=20), erythema nodosum 24.1%(n=13) respectively. Bilateral uveitis was found in 27.8% (n=15) patients. Pathergy phenomen was positive in 37% (n=20) patients. Family history of BD was present in 38.9% (n=21) patients. HLA-B51 carrier rate was 53.7% (n=29). BSAS was assessed for the 52 patients in our cohort and a moderate correlation between the BSAS and PGA was demonstrated (r=0.305, p=0.025).
منابع مشابه
Behçet disease – although rare can be present in children
Introduction The child’s history reveals frequent faringitis accompanied by oral lesions (4-5 episodes/year), billatreal ankle joint swelling and weight loss. Behçet disease (BD) is characterized by a triple-symptom complex of recurrent oral aphthous ulcers, genital ulcers, and uveitis. Hippocrates may have described Behçet disease in the fifth century BC; however, the first description of the ...
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